Primary“Botryoid”Embryonal   Rhabdomyosarcoma in Mesentery

　　肠系膜原发’葡萄状’胚胎型横纹肌肉瘤

　　Rhabdomyosarcoma is a soft tissue neoplasm arising from primitive embryonal mesenchyma. Embryonal rhabdomyosarcoma mostly affects children younger than 10 years of age, but it also occurs in adolescents and young adults. Pleomorphic rhabdomyosarcoma is a rare variant that almost always arises in adults older than 45 years of age. Mesentery is a rare site for botyroid embryonal rhabdomyosarcoma and on extensive search we found only one case of a botryoid rhabdomyosarcoma in a child of 2 years. We report a rare case of botyroid embryonal rhabdomyosarcoma occurring in the mesentery of a 30 year old female.

　　横纹肌肉瘤是起源于原始胚胎间叶细胞的一种软组织恶性肿瘤。胚胎横纹肌肉瘤最影响<10岁的儿童，但是同样发生在青少年和青壮年身上。多形性横纹肌肉瘤主要发生于成人，多见于45岁以上。  葡萄状胚胎型横纹肌肉瘤原发于肠系膜罕见，大量的研究仅发现一例二岁孩子罹患葡萄状胚胎型横纹肌肉瘤 。很少报道关于30岁成熟女性罹患这种葡萄状胚胎状横纹肌肉瘤。